Encapsulating sclerosingperitonitis : two Rare observations and literature review.

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Houcine Maghrebi
Amine Makni
Rami Rhaeim
Alia Zehani
Anis Haddad
Amine Daghfous
Wael Rebai
Mohamed Jouini
Montasser Kacem
Zoubeir Ben Safta

Abstract

Sclerosing encapsulating peritonitis (SEP) is a rare and little known pathological entity. It is a chronic fibro-inflammatory disease of the peritoneum, resulting in the formation of a thick fibrous membrane, which engages partially or totally the abdominal organs. Clinical and radiological signs make the diagnosis difficult to establish preoperatively. We present two original observations of SEP illustrating different clinical presentations, diagnostic and therapeutic means. His diagnosis requires a peritoneal biopsy. The treatment is not completely established. Surgical treatment is difficult, involving viscerolysis and multiple incisions of the fibrous membrane. Despite the current progress in therapeutic management, the prognosis remains pejorative, with significant mortality.

Keywords:

Sclerosing encapsulating peritonitis, imaging, surgery

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