Primary Ewing’s sarcoma of the sphenoid sinus with orbital and intracranial extension: a case report

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Senda Turki
Skander Kedous
Madiha Mahjoubi
Sawssen Dhambri
Zied Attia
Slim Touati

Abstract

Background : Ewing's sarcoma is a high-grade neuroectodermal primary bone tumor. This is the second primary bone tumor in children afterosteosarcoma and represents 4 to10% of cases. It can occur in all skeletal bones. However, the location at the facial bones is uncommon (1to2%) and extremely rare at the sphenoid sinus. We report the clinical results of a rare case of Ewing's sarcoma of the sphenoid with intraorbitaland intracranial extension.

Keywords:

Ewing's sarcoma, sphenoid sinus, orbit, intracranial, chemotherapy

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References

  1. Ben Hassinea L., Hedhlia M., Douira W. et al. Tuméfaction jugale d'évolution chronique chez un adolescent. Feuillets de radiologie 2010;50:319-23
  2. Sharma A., Garg A., Mishra N. K. and al. Primary Ewing's sarcoma of the sphenoid bone with unusual imaging features: a case report. Clin Neurol Neurosurg. 2005; 107: 528-31.
  3. Vaccani J.P., Forte V., De Jong A.L., Taylor G. Ewing's sarcoma of the head and neck in children. Int J Pediatr Otorhinolaryngol 1999; 25:209-16
  4. Gupta S., Gupta O.P., Mehrotra S., Mehrotra D. Ewing's sarcoma of the maxilla: a rare presentation. Quintessence int 2009;40:135-40.
  5. Amin M.N., Islam K.M., Ahmed A.N. and al. Ewing's sarcoma of maxilla: a case report. Bangladesh Med. Res. Counc. Bull 1990;16:42-5.
  6. Li M., Hoschar A.P., Budd G.T. et al. Primary Ewing's sarcoma of the ethmoid sinus with intracranial and orbital extension: case report and literature review. Am J Otolaryngol 2013; 34:563-8.
  7. Kaler A.K., Sheriff S. Primary Ewing's sarcoma of the paranasal sinuses and orbit. Innov J Med Health Sci 2013; 3:1-3.
  8. Woodruff G., Thorner P., Skarf B. Primary Ewing's sarcoma of the orbit presenting with visual loss. Br J Ophtalmol 1988;72:786-92.
  9. Civit T., Freppel S., Baylac F. Tumeurs primitives des parois osseuses orbitaires. Neurochirurgie 2010 ; 56 :165-73.
  10. Li W., Huang J.T., Chen X.Q. et al. Extraosseous Ewing's sarcoma arising from the pterygomandibular space. Open Journal of Stomatologie 2011;1:114-120.
  11. Casiraghi O., Lefèvre M. Tumeurs malignes indifférenciées à cellules rondes des cavités nasosinusiennes et du nasopharynx. Ann Pathol 2009 ;29 :296-312.
  12. Pawar V.R., More S., Patil P.P. Cytological diagnosis of Ewing sarcoma clavicle. Indian Med Gaz 2011: CLXV:495-7.