Congenital Cystic Adenomatoid Malformation of the lung: two cases report

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Published Jan 18, 2011
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Vol. 89 No. 1 (2011): Issue Jan 2011

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Sihem Chaouachi
Emira Ben Hamida
Nedia Ben Fraj
Sonia Blibèche
Zahra Marrakchi

Abstract

Background: Congenital cystic adenomatoid malformation (CCAM) is a rare embryonic developmental abnormality with an incidence of one in 25 000 to 35 000 pregnancies. With advances in antenatal ultrasonographia (USG), CCAM has been increasingly diagnosed. After birth, the clinical appearance of CCAM can vary from immediately postnatal respiratory distress, to an incidental finding on chest radiography.
Aim: To report two additional cases with CCAM different in clinical features.
Case reports: The first case was a boy in witch diagnosis was suspected by antenatal USG; he was born at 37 weeks of gestation by cesarean section because of severe toxemia, and presented immediately respiratory distress. The chest x ray and computed tomography scan (CT scan) revealed a right CCAM.
The second case was also a boy of an inducted threefold pregnancy, born at 30 weeks by cesarean section. He presented immediately respiratory distress. The diagnosis of a right CCAM was confirmed by clinical and radiological findings in postnatal period.
Conclusion: The two cases described in this report show the disparity in clinical features of CCAM. Nowadays, antenatal echotomography can establish the diagnosis allowing optimum management.

Keywords:

Antenatal ultrasonography,, congenital cystic adenomatoid malformation, newborn

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