Ear nose sarcoma. Reprt of 3 cases

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Published May 31, 2010
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Vol. 88 No. 6 (2010): Issue Jun 2010

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Sethom A
Akkari K
Hachicha A
Bahri W
Miled I
Benzarti S
Kamel Chebbi M

Abstract

Background : Head and neck sarcoma are very rare malignant tumors which can occur on any different ENT localization.
Aim : The authors report tree different variety of ENT sarcoma diagnosed and treated at the oto-rhino-laryngological department of military hospital of Tunis. We intend to remind of clinical and histological particularities, therapeutic modalities and finally to evaluate the follow-up.
Methods: From 2001 to 2007, three cases of head and neck sarcomas were diagnosted in ENT department of military hospital of Tunis.
Results: the study concerned a women (22 years old) and two men 36 and 76 years old. It deals with an orbital rhabdomyosarcoma, a carcinosarcoma of submandibular gland and a maxillary chondrosarcoma. In each case, diagnosis was validated by the immunohistochemistry. All patients had surgical removal of their tumor. External irradiation or/and chemotherapy was also indicated for all cases.
Conclusion: ENT sarcomas are aggressive neoplasm. Long-term survival is bad with high potentialities of local recurrence and distant metastases.

Keywords:

rhabdomyosarcoma, chondrosarcoma, carcinosarcoma

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