Catecholaminergic Polymorphic Ventricular Tachycardia In Adult: A Case Report
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Abstract
Background : Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a primary electrical myocardial disease characterized by exercise- and stress-related ventricular lachycardia manifested as syncope and sudden death usually in child and teenager and was rarely described in adults. The management
includes betablockade, with the use of implantable cardioverter defibrillators if medical treatment is insufficient.
Aim : Report a new case of CPVT.
Observation : We report a case of a 43 years old patient in whom CPVT diagnosis was made during his exploration for palpitations occurring with the effort. Registration Holter ECG revealed several episodes of supraventricular tachycardia and episodes of nocturnal sino-atrial block. The patient had an ICD and betablockade treatment.
Conclusion: The TVPC in adult can manifest with attenuated symptoms that can be summarized with palpitations with the exertion. The supraventricular arrhythmias and sinus dysfunction may be at the forefront of Electrocardiographic manifestations. The prognosis of this form seems better than the TVPC of the child. Treatment with betablockade appears to be effective but existing dysfunction sinus facilitates decision to implant the ICD.
Keywords:
Catecholaminergic polymorphic ventricular tachycardia, sudden cardiac death, supraventricular tachycardia, syncope, Implantable Cardioverter Defibrillator##plugins.themes.academic_pro.article.details##
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