Rare localisation of sarcoma of the child: Thoracic ewing sarcoma

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Published Apr 3, 2010
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Vol. 88 No. 4 (2010): Issue Apr 2010

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Leila El Fekih
Hela Hassene
Hajer Abdelghaffar
Sorraya Fenniche
Dalenda Belhabib
Service de pneumologie Ibn Nafiss. Hôpital Abderrhmane MAMI de L'ARIANA
Khaoula Ben Miled
Faouzi Mezni
Mohamed Lamine Megdiche

Abstract

Background: Ewing Sarcoma is considered as primitive neuro ectodermic tumor. It’s the most frequent osseous tumor in children and adolescent. It was localised frequently at long osseous and pelvis, however, it can be arising from the rib.
Aim : this article aimed to show that Ewing sarcome could arise twely from thorax.
Case report: We report the case of 15-year-old girl, admitted in our hospital because of left scapular pain with important weight loss. Chest X ray showed dense left latero tracheal opacity with mediastinal limits. Bronchofiberoscopy was performed and it showed no abnormalities. Thoracic CT scan and MRI noted left posteroir expansif mediastinal process infiltrating D2, D3 and homolateral conjugation’s canal. This process was associated at vertebral metastasis in D1, D4 and D8.Rapid clinical aggravation, with installation for medullar compression was noted. The patient had benefit for three cures of decompress radiotherapy and treated by laminectomy of dorsal vertebras in neurosurgery department. Morphologic aspects and immunohistochimical study for the operator piece concluded at Ewing sarcoma of the children considered as primitive neuro ectodermic tumor. Six cures of chemotherapy had been prescribed with well recuperation of the motor failure. She still on life since 7 months
Conclusion: Even rare, thoracic localisation of Ewing sarcoma in not exceptional, it is necessary to evocate it in front of mediastinal mass.

Keywords:

Sarcoma, Ewing, Thorax, Rib

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