LOCALIZED SCLERODERMA : A RETROSPECTIVE STUDY ABOUT 92 CASES

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Published Dec 3, 2009
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Vol. 87 No. 9 (2009): Issue Sep 2009

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Nadia El Fékih
Iméne réjaibi
Hajer Kamoun
Faten Zéglaoui
Bécima Fazaa
Monia Kharfi
Mohamed Ridha Kamoun

Abstract

Background : Sclerodermas are rare affections which can be located or generalized. Localized form is the most frequent.
Aim : The purpose of this study was to describe epidemiologic, clinics, biological, immunological, therapeutic, evolutionary characteristics of the localized scleroderma through a personal series and the data of the literature
Method: We have performed a retrospective study on all patients followed in the department of dermatology of the Hospital Charles Nicole during 14 years period.
Results: Our study was about 92 cases of localized scleroderma (73 were females and 19 males). The mean age was 35 years (between 2 and 72 years). The majority of localised sclerodermas (66,2% of the cases) appeared before 40 years with a maximum of frequency between 10 and 30 years (41,6%). Only 11.9% of  the cases wereobserved before 10 years. They were 51 cases (55%) of morphea, 35 cases (38%) of scleroderma in bands including 32 linear scleroderma
and 3 scleroderma en coup de sabre, 5 cases (5,5%) of generalizedmorphea and 1 case (0,15%) of deep morphea. Average therapeutic was specified among 63 patients (87 %), and the evolution could be appreciated among 45 patients.
Conclusion : The epidemiologic data observed in our series are comparable with those reported in the literature. Therapeutic difficulties and risks of functional after-effects, particular in scleroderma in bands, remain the principal concern for all the authors.

Keywords:

Localized scleroderma, morphea

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